The Chapel Hill Consensus Conferences (CHCC) (1994 and 2012) are a pair of international conferences which addressed the need of standardized classification system for systemic vasculitides.
2012 Revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides
| Classification Group | Diseases |
|---|---|
| Large-vessel vasculitis (LVV) | Takayasu's arteritis (TAK); Giant-cell arteritis (GCA) |
| Medium-vessel vasculitis (MVV) | Polyarteritis nodosa (PAN), Kawasaki disease (KD) |
| Small vessel vasculitis (SVV) | ANCA-associated vasculitis (AAV); Immune complex SVV |
| Variable vessel vasculitis (VVV) | Behcet's disease (BD); Cogan's syndrome (CS) |
| Single Organ Vasculitis (SOV) | Cutaneous leukocytoclastic angiitis; cutaneous arteritis; primary central nervous system vasculitis; isolated aortitis; others |
| Vasculitis associated with systemic disease | Lupus vasculitis; Rheumatoid vasculitis; Sarcoid vasculitis; others |
| Vasculitis associated with probable etiology | Hepatitis C virus-associated cryoglobulinemic vasculitis; Hepatitis B virus-associated vasculitis; Syphilis-associated aortitis; Drug-associated immune complex vasculitis; Cancer-associated vasculitis; others |
References
- Jennette JC; Nomenclature of systemic vasculitides. Proposal of an international consensus conference; Arthritis Rheum 2013
- Jennette, JC; Overview of the 2012 Revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides; Clinical and Experimental Nephrology, 2013