Congenital self-healing reticulohistiocytosis

(Redirected from Hashimoto-Pritzker disease) Medical condition

Congenital self-healing reticulohistiocytosis
Other names	Hashimoto–Pritzker disease, and Hashimoto–Pritzker syndrome
Specialty	Dermatology

Congenital self-healing reticulohistiocytosis is a condition that is a self-limited form of Langerhans cell histiocytosis.

Symptoms

Non-specific inflammatory response, which includes fever, lethargy, and weight loss. This is suspected of being a genetic disorder, and as the name implies, is self healing.

Skin: Commonly seen are a rash which varies from scaly erythematous lesions to red papules pronounced in intertriginous areas. Up to 80% of patients have extensive eruptions on the scalp.
Lymph node: Enlargement of the lymph nodes in 50% of Histiocytosis cases.

Diagnosis

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Treatment

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History

It was first described by Ken Hashimoto and M. S. Pritzkar in 1973.

References

Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 978-1-4160-2999-1.
^ James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. ISBN 978-0-7216-2921-6.
"Langerhans Cell Histiocytosis - Patient UK". Archived from the original on 2012-02-12. Retrieved 2007-05-10.
John Thorne Crissey; Lawrence C. Parish; Karl Holubar (2013). Historical Atlas of Dermatology and Dermatologists. CRC Press. p. 179. ISBN 978-1-84214-100-7.
Lee, Young H.; Talekar, Mala K.; Chung, Catherine G.; Bell, Moshe D.; Zaenglein, Andrea L. (February 2014). "Congenital Self-Healing Reticulohistiocytosis". The Journal of Clinical and Aesthetic Dermatology. 7 (2): 49–53. ISSN 1941-2789. PMC 3935651. PMID 24578781.

External links

Classification	D MeSH: C535843
External resources	eMedicine: article/1336764

v t e Histiocytosis
WHO-I/Langerhans cell histiocytosis/ X-type histiocytosis	Letterer–Siwe disease Hand–Schüller–Christian disease Eosinophilic granuloma Congenital self-healing reticulohistiocytosis
WHO-II/non-Langerhans cell histiocytosis/ Non-X histiocytosis	Juvenile xanthogranuloma Hemophagocytic lymphohistiocytosis Erdheim-Chester disease Niemann–Pick disease Sea-blue histiocytosis Benign cephalic histiocytosis Generalized eruptive histiocytoma Xanthoma disseminatum Progressive nodular histiocytosis Papular xanthoma Hereditary progressive mucinous histiocytosis Reticulohistiocytosis (Multicentric reticulohistiocytosis, Reticulohistiocytoma) Indeterminate cell histiocytosis
WHO-III/malignant histiocytosis	Histiocytic sarcoma Langerhans cell sarcoma Interdigitating dendritic cell sarcoma Follicular dendritic cell sarcoma
Ungrouped	Rosai–Dorfman disease

Category:

Monocyte- and macrophage-related cutaneous conditions

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