Unilateral nevoid telangiectasia

Medical condition

Unilateral nevoid telangiectasia
Specialty	Dermatology

Unilateral nevoid telangiectasia presents with fine thread veins, typically over a segment of skin supplied by a particular nerve on one side of the body. It most frequently involves the trigeminal, C3 and C4, or nearby areas. The condition was named in 1970 by Victor Selmanowitz.

Signs and symptoms

Unilateral nevoid telangiectasia is characterized by multiple chronic asymptomatic superficial blanching telangiectasias along dermatomes or Blaschko's lines, with asymmetric skin involvement, while symmetric instances have been infrequently recorded. The trunk and upper extremities' third and fourth cervical dermatomes are the most severely impacted.

Causes

Unilateral nevoid telangiectasia can be congenital or acquired. Rare congenital type manifests at or soon after the neonatal period; it is more common in males and occurs in an autosomal dominant pattern. Conversely, the acquired form is nearly exclusively found in young female patients who have physiologic problems.

Diagnosis

A normal-appearing epidermis with superficial dermal telangiectatic blood vessels beneath and a low level of inflammatory infiltration is revealed by histopathologic investigation.

Treatment

After the triggering factor is eliminated, unilateral nevoid telangiectasia usually persists but in rare situations, it resolves on its own. The first step in treatment is cosmetic concealment. The condition has improved aesthetically with the use of pulsed dye laser, which has proven to be a useful alternative.

References

^ James, William D.; Elston, Dirk; Treat, James R.; Rosenbach, Misha A.; Neuhaus, Isaac (2020). "28. Dermal and subcutaneous tumors: Unilateral nevoid telangiectasia". Andrews' Diseases of the Skin: Clinical Dermatology (13th ed.). Edinburgh: Elsevier. pp. 604–605. ISBN 978-0-323-54753-6.
Mulliken, John B. (2013). "13. Capillary malformations, hyperkeratotic stains, telangiectasias, and miscellaneous vascular blots". In Mulliken, John B.; Burrows, Patricia E.; Fishman, Steven J. (eds.). Mulliken and Young's Vascular Anomalies: Hemangiomas and Malformations (2nd ed.). Oxford University Press. p. 544. ISBN 978-0-19-972254-9.
Akman-Karakaş, A.; Kandemir, H.; Senol, U.; Unal, A.; Duman, O.; Ciftcioglu, M.A.; Haspolat, S.; Alpsoy, E. (2011-12-21). "Authors reply: New clues on the path of understanding unilateral naevoid telangiectasia". Journal of the European Academy of Dermatology and Venereology. 27 (2). Wiley: 258–259. doi:10.1111/j.1468-3083.2011.04408.x. ISSN 0926-9959. PMID 22188514.
^ Abbas, O.; Rubeiz, N.; Ghosn, S. (2010). "Extensive and progressive eruption in a young woman". Clinical and Experimental Dermatology. 35 (3). Oxford University Press (OUP): e85–e86. doi:10.1111/j.1365-2230.2009.03547.x. ISSN 0307-6938. PMID 20500195.
Happle, R. (2015-04-10). "Capillary malformations: a classification using specific names for specific skin disorders". Journal of the European Academy of Dermatology and Venereology. 29 (12). Wiley: 2295–2305. doi:10.1111/jdv.13147. ISSN 0926-9959. PMID 25864701.
Erbagci, Z; Erbagci, I; Erkiliç, S; Bekir, Na (2004-02-19). "Angioma serpiginosum with retinal involvement in a male: a possible aetiological role of continuous cold exposure". Journal of the European Academy of Dermatology and Venereology. 18 (2). Wiley: 238–239. doi:10.1111/j.1468-3083.2004.00899.x. ISSN 0926-9959. PMID 15009324.
^ Guedes, Rita; Leite, L (2012). "Unilateral nevoid telangiectasia: A rare disease?". Indian Journal of Dermatology. 57 (2). Medknow: 138. doi:10.4103/0019-5154.94288. ISSN 0019-5154. PMC 3352640. PMID 22615515.
Afsar, FSule; Ortac, Ragip; Diniz, Gulden (2008). "Unilateral nevoid telangiectasia with no estrogen and progesterone receptors in a pediatric patient". Indian Journal of Dermatology, Venereology and Leprology. 74 (2). Scientific Scholar: 163–164. doi:10.4103/0378-6323.39712. hdl:1807/48090. ISSN 0378-6323. PMID 18388386.
Hynes, Lisa R.; Shenefelt, Phillip D. (1997). "Unilateral nevoid telangiectasia: Occurrence in two patients with hepatitis C". Journal of the American Academy of Dermatology. 36 (5). Elsevier BV: 819–822. doi:10.1016/s0190-9622(97)70030-6. ISSN 0190-9622.

External links

Classification	D ICD-11: LC50.Y ICD-10: I78.8 DiseasesDB: 31389 SNOMED CT: 767127000
External resources	eMedicine: article/1085019 Scholia: Q7885201

v t e Cutaneous vasculitis and other vascular-related cutaneous conditions
Cutaneous vasculitis	Erythema elevatum diutinum Capillaritis Urticarial vasculitis Nodular vasculitis
Microvascular occlusion	Calciphylaxis Cryoglobulinemic purpura/Cryoglobulinemic vasculitis vascular coagulopathy: Livedoid vasculopathy Livedoid dermatitis Perinatal gangrene of the buttock Malignant atrophic papulosis Sneddon's syndrome
Purpura	Nonthrombocytopenic purpura: Cryofibrinogenemic purpura Drug-induced purpura Food-induced purpura IgA vasculitis Obstructive purpura Orthostatic purpura Purpura fulminans Purpura secondary to clotting disorders Purpuric agave dermatitis Pigmentary purpuric eruptions Solar purpura Traumatic purpura Waldenström hyperglobulinemic purpura Painful bruising syndrome ungrouped: Paroxysmal hand hematoma Postcardiotomy syndrome Deep vein thrombosis Superficial thrombophlebitis Mondor's disease Blueberry muffin baby Fibrinolysis syndrome
Systemic vasculitis	see Template:Systemic vasculitis
Vascular malformations	Arteriovenous malformation Bonnet–Dechaume–Blanc syndrome Cobb syndrome Parkes Weber syndrome Sinusoidal hemangioma lymphatic malformation Hennekam syndrome Aagenaes syndrome telangiectasia: Generalized essential telangiectasia Hereditary hemorrhagic telangiectasia Unilateral nevoid telangiectasia
Ulcer	Venous ulcer Arterial insufficiency ulcer Hematopoietic ulcer Neuropathic ulcer Acroangiodermatitis
Lymphedema	see Template:Lymphatic vessel disease
Ungrouped vascular-related cutaneous conditions	Raynaud's phenomenon Thromboangiitis obliterans Erythromelalgia Septic thrombophlebitis Arteriosclerosis obliterans Bier spots/Marshall–White syndrome Cholesterol embolus Reactive angioendotheliomatosis Trousseau's syndrome

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