Pigmented purpuric dermatosis

Medical condition

Pigmented purpuric dermatosis
Other names	Progressive pigmentary dermatosis, Purpura pigmentosa chronica, Pigmentary purpuric eruptions, or Progressive pigmenting purpura or Schamberg's disease

Specialty	Dermatology

Pigmented purpuric dermatosis refers to one of the three major classes of skin conditions characterized by purpuric skin eruptions.

Pigmented purpuric dermatosis are distinguished from other purpura by size (0.3–1 cm) and are most often seen in the lower extremities. Pigmentary purpuric eruptions may present with one of several clinical patterns. There may be overlapping characteristics among pigmented purpuric dermatosis and between their signs and those of other purpuric eruptions. Examples of the pigmented purpuric dermatosis group include:

Schamberg's disease
Majocchi's disease (Purpura annularis telangiectodes)
Gougerot-Blum syndrome (Pigmented purpuric lichenoid dermatitis)
Ducas and Kapetanakis pigmented purpura
Lichen aureus

Although vascular damage may be present, it is insufficient for these conditions to be considered forms of vasculitis.

A few very small non-blinded studies of treatment with narrow-band ultraviolet light have been reported as promising.

References

^ James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. ISBN 978-0-7216-2921-6.
David E. Elder; Rosalie Elenitsas; Michael D Ioffreda; Bernett L. Johnson, Jr. (2007). Atlas and synopsis of Lever's histopathology of the skin. Lippincott Williams & Wilkins. pp. 127–. ISBN 978-0-7817-6845-0. Retrieved 22 May 2010.
Summarized in 2015 by Tapan Kumar Dhali, Monica Chahar, and Mohammad Asad Haroon in Phototherapy as an effective treatment for Majocchi's disease - Case report An Bras Dermatol. 2015 Jan-Feb; 90(1): 96–99. doi:10.1590/abd1806-4841.20153067 PMC 4323703 PMID 25672304

External links

Classification	D ICD-10: L81.7 OMIM: 172900 MeSH: C537186 DiseasesDB: 30753
External resources	eMedicine: article/1084594

Pigmentation disorders/Dyschromia

Hypo-/
leucism

Loss of
melanocytes

Vitiligo	Quadrichrome vitiligo Vitiligo ponctué
Syndromic	Alezzandrini syndrome Vogt–Koyanagi–Harada syndrome
Melanocyte development	Piebaldism Waardenburg syndrome Tietz syndrome

Loss of melanin/
amelanism

Albinism	Oculocutaneous albinism Ocular albinism in humans
Melanosome transfer	Hermansky–Pudlak syndrome Chédiak–Higashi syndrome Griscelli syndrome Elejalde syndrome Griscelli syndrome type 2 Griscelli syndrome type 3
Other	Cross syndrome ABCD syndrome Albinism–deafness syndrome Idiopathic guttate hypomelanosis Phylloid hypomelanosis Progressive macular hypomelanosis

Leukoderma w/o
hypomelanosis

Ungrouped

Hyper-

Melanin/
Melanosis/
Melanism

Reticulated	Dermatopathia pigmentosa reticularis Pigmentatio reticularis faciei et colli Reticulate acropigmentation of Kitamura Reticular pigmented anomaly of the flexures Naegeli–Franceschetti–Jadassohn syndrome Dyskeratosis congenita X-linked reticulate pigmentary disorder Galli–Galli disease Revesz syndrome
Diffuse/ circumscribed	Lentigo/Lentiginosis: Lentigo simplex Liver spot Centrofacial lentiginosis Generalized lentiginosis Inherited patterned lentiginosis in black persons Ink spot lentigo Lentigo maligna Mucosal lentigines Partial unilateral lentiginosis PUVA lentigines Melasma Erythema dyschromicum perstans Lichen planus pigmentosus Café au lait spot Poikiloderma (Poikiloderma of Civatte Poikiloderma vasculare atrophicans) Riehl melanosis
Linear	Incontinentia pigmenti Scratch dermatitis Shiitake mushroom dermatitis
Other/ ungrouped	Acanthosis nigricans Freckle Familial progressive hyperpigmentation Pallister–Killian syndrome Periorbital hyperpigmentation Photoleukomelanodermatitis of Kobori Postinflammatory hyperpigmentation Transient neonatal pustular melanosis

Other
pigments

Iron	Hemochromatosis Iron metallic discoloration Pigmented purpuric dermatosis Schamberg disease Majocchi's disease Gougerot–Blum syndrome Doucas and Kapetanakis pigmented purpura/Eczematid-like purpura of Doucas and Kapetanakis Lichen aureus Angioma serpiginosum Hemosiderin hyperpigmentation
Other metals	Argyria Chrysiasis Arsenic poisoning Lead poisoning Titanium metallic discoloration
Other	Carotenosis Tar melanosis

Dyschromia

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